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Ubiquitin-proteasome-rich cytoplasmic structures in neutrophils of patients with Shwachman-Diamond syndrome

BACKGROUND: Shwachman–Diamond syndrome is an autosomal recessive disorder in which severe bone marrow dysfunction causes neutropenia and an increased risk of leukemia. Recently, novel particulate cytoplasmic structures, rich in ubiquitinated and proteasomal proteins, have been detected in epithelial...

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Hlavní autoři: Necchi, Vittorio, Minelli, Antonella, Sommi, Patrizia, Vitali, Agostina, Caruso, Roberta, Longoni, Daniela, Frau, Maria Rita, Nasi, Cristina, De Gregorio, Fabiola, Zecca, Marco, Ricci, Vittorio, Danesino, Cesare, Solcia, Enrico
Médium: Artigo
Jazyk:Inglês
Vydáno: Ferrata Storti Foundation 2012
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On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC3396678/
https://ncbi.nlm.nih.gov/pubmed/22271888
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3324/haematol.2011.048462
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