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Ubiquitin-proteasome-rich cytoplasmic structures in neutrophils of patients with Shwachman-Diamond syndrome

BACKGROUND: Shwachman–Diamond syndrome is an autosomal recessive disorder in which severe bone marrow dysfunction causes neutropenia and an increased risk of leukemia. Recently, novel particulate cytoplasmic structures, rich in ubiquitinated and proteasomal proteins, have been detected in epithelial...

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Detalhes bibliográficos
Main Authors: Necchi, Vittorio, Minelli, Antonella, Sommi, Patrizia, Vitali, Agostina, Caruso, Roberta, Longoni, Daniela, Frau, Maria Rita, Nasi, Cristina, De Gregorio, Fabiola, Zecca, Marco, Ricci, Vittorio, Danesino, Cesare, Solcia, Enrico
Formato: Artigo
Idioma:Inglês
Publicado em: Ferrata Storti Foundation 2012
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3396678/
https://ncbi.nlm.nih.gov/pubmed/22271888
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3324/haematol.2011.048462
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