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Pathological Roles of Wild-Type Cu, Zn-Superoxide Dismutase in Amyotrophic Lateral Sclerosis

Dominant mutations in a Cu, Zn-superoxide dismutase (SOD1) gene cause a familial form of amyotrophic lateral sclerosis (ALS). While it remains controversial how SOD1 mutations lead to onset and progression of the disease, many in vitro and in vivo studies have supported a gain-of-toxicity mechanism...

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Detalles Bibliográficos
Autor Principal: Furukawa, Yoshiaki
Formato: Artigo
Idioma:Inglês
Publicado: Hindawi Publishing Corporation 2012
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3395178/
https://ncbi.nlm.nih.gov/pubmed/22830015
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2012/323261
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