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Peroxisomal L-bifunctional enzyme (Ehhadh) is essential for the production of medium-chain dicarboxylic acids

L-bifunctional enzyme (Ehhadh) is part of the classical peroxisomal fatty acid β-oxidation pathway. This pathway is highly inducible via peroxisome proliferator-activated receptor α (PPARα) activation. However, no specific substrates or functions for Ehhadh are known, and Ehhadh knockout (KO) mice d...

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Bibliografski detalji
Glavni autori: Houten, Sander M., Denis, Simone, Argmann, Carmen A., Jia, Yuzhi, Ferdinandusse, Sacha, Reddy, Janardan K., Wanders, Ronald J. A.
Format: Artigo
Jezik:Inglês
Izdano: The American Society for Biochemistry and Molecular Biology 2012
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC3371241/
https://ncbi.nlm.nih.gov/pubmed/22534643
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.M024463
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