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Recognition of Tuberous Sclerosis in Adult Women: Delayed Presentation With Life-Threatening Consequences

BACKGROUND: Tuberous sclerosis complex (TSC) is associated with tumor development in the brain, retina, kidney, skin, heart, and lung. Seizures, intellectual disability, and characteristic skin lesions commonly manifest in early childhood, but some findings, notably renal angiomyolipomas and pulmona...

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Autors principals: Seibert, Diane, Hong, Chien-Hui, Takeuchi, Fumiko, Olsen, Cara, Hathaway, Olonda, Moss, Joel, Darling, Thomas N.
Format: Artigo
Idioma:Inglês
Publicat: 2011
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3367307/
https://ncbi.nlm.nih.gov/pubmed/21690595
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1059/0003-4819-154-12-201106210-00008
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