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Pseudoxanthoma Elasticum: Oxidative Stress and Antioxidant Diet in a Mouse Model (Abcc6(−/−))

Pseudoxanthoma elasticum (PXE), a multi-system disorder characterized by ectopic mineralization of soft connective tissues, is caused by mutations in the ABCC6 gene. The pathomechanistic details of the mineralization process are largely unknown, but oxidative stress has been suggested to play a role...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Li, Qiaoli, Jiang, Qiujie, Uitto, Jouni
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2007
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3357057/
https://ncbi.nlm.nih.gov/pubmed/18049453
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/sj.jid.5701145
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