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Loss of Emerin Alters Myogenic Signaling and miRNA Expression in Mouse Myogenic Progenitors

Emerin is an integral membrane protein of the inner nuclear membrane. Mutations in emerin cause X-linked Emery-Dreifuss muscular dystrophy (EDMD), a disease characterized by skeletal muscle wasting and dilated cardiomyopathy. Current evidence suggests the muscle wasting phenotype of EDMD is caused b...

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Autors principals: Koch, Adam J., Holaska, James M.
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2012
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3350500/
https://ncbi.nlm.nih.gov/pubmed/22606356
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0037262
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