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An inherited enzymatic defect in porphyria cutanea tarda: decreased uroporphyrinogen decarboxylase activity.

Uroporphyrinogen decarboxylase activity was measured in liver and erythrocytes of normal subjects and in patients with porphyria cutanea tarda and their relatives. In patients with porphyria cutanea tarda, hepatic uroporphyrinogen decarboxylase activity was significantly reduced (mean 0.43 U/mg prot...

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Detaylı Bibliyografya
Asıl Yazarlar: Kushner, J P, Barbuto, A J, Lee, G R
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 1976
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC333275/
https://ncbi.nlm.nih.gov/pubmed/993332
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