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Interactions of spectrin in hereditary elliptocytes containing truncated spectrin beta-chains.

An abnormal spectrin, in which one subunit is truncated, has been detected in a large German family. The inheritance is autosomal dominant. The affected members of the family suffer in widely varying degree from a microcytic hemolytic anemia. The red cell morphology varies correspondingly from smoot...

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Dettagli Bibliografici
Autori principali: Eber, S W, Morris, S A, Schröter, W, Gratzer, W B
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1988
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC329600/
https://ncbi.nlm.nih.gov/pubmed/3276733
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