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Molecular Diagnostic and Pathogenesis of Hereditary Hemochromatosis

Hereditary hemochromatosis (HH) is an autosomal recessive disorder characterized by enhanced intestinal absorption of dietary iron. Without therapeutic intervention, iron overload leads to multiple organ damage such as liver cirrhosis, cardiomyopathy, diabetes, arthritis, hypogonadism and skin pigme...

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Autori principali: Santos, Paulo C. J. L., Krieger, Jose E., Pereira, Alexandre C.
Natura: Artigo
Lingua:Inglês
Pubblicazione: Molecular Diversity Preservation International (MDPI) 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3291973/
https://ncbi.nlm.nih.gov/pubmed/22408404
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms13021497
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