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Enhancing translation: guidelines for standard pre-clinical experiments in mdx mice

Duchenne Muscular Dystrophy is an X-linked disorder that affects boys and leads to muscle wasting and death due to cardiac involvement and respiratory complications. The cause is the absence of dystrophin, a large structural protein indispensable for muscle cell function and viability. Neither an ef...

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Dettagli Bibliografici
Autori principali: Willmann, Raffaella, De Luca, Annamaria, Benatar, Michael, Grounds, Miranda, Dubach, Judith, Raymackers, Jean-Marc, Nagaraju, Kanneboyina
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2011
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3227750/
https://ncbi.nlm.nih.gov/pubmed/21737275
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.nmd.2011.04.012
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