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Deficient activity of dephosphophosphorylase kinase and accumulation of glycogen in the liver

Low activity of phosphorylase and increased concentration of glycogen were found in liver tissue from five children with asymptomatic hepatomegaly. In vitro activation of liver phosphorylase in these patients occurred at the rate of 10% or less of normal. Elimination of the defect by the addition of...

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Détails bibliographiques
Publié dans:J Clin Invest
Auteurs principaux: Hug, George, Schubert, William K., Chuck, Gail
Format: Artigo
Langue:Inglês
Publié: American Society for Clinical Investigation 1969
Sujets:
Accès en ligne:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC322275/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/5774108/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI106028
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