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Update of Respiratory Tract Disease in Children with Primary Ciliary Dyskinesia
Primary ciliary dyskinesia (PCD) is a rare genetic disease characterized by abnormal ciliary structure and function leading to impaired mucociliary clearance and chronic progressive sinopulmonary disease. Upper and lower respiratory tract manifestations are cardinal features of PCD. This review summ...
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Autori principali: | , , , |
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Natura: | Artigo |
Lingua: | Inglês |
Pubblicazione: |
American Thoracic Society
2011
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Soggetti: | |
Accesso online: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3209579/ https://ncbi.nlm.nih.gov/pubmed/21926396 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1513/pats.201103-024SD |
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