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Update of Respiratory Tract Disease in Children with Primary Ciliary Dyskinesia

Primary ciliary dyskinesia (PCD) is a rare genetic disease characterized by abnormal ciliary structure and function leading to impaired mucociliary clearance and chronic progressive sinopulmonary disease. Upper and lower respiratory tract manifestations are cardinal features of PCD. This review summ...

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Autors principals: Sagel, Scott D., Davis, Stephanie D., Campisi, Paolo, Dell, Sharon D.
Format: Artigo
Idioma:Inglês
Publicat: American Thoracic Society 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3209579/
https://ncbi.nlm.nih.gov/pubmed/21926396
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1513/pats.201103-024SD
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