Loading...

Reduced secretion of structurally abnormal type I procollagen in a form of osteogenesis imperfecta.

Osteogenesis imperfecta is a clinically and genetically heterogeneous group of inherited connective tissue disorders in which bone fragility is the predominant feature. Cultured dermal fibroblasts from one patient with the lethal perinatal form of osteogenesis imperfecta secrete type I procollagen a...

Fuld beskrivelse

Na minha lista:
Bibliografiske detaljer
Udgivet i:Proc Natl Acad Sci U S A
Main Authors: Barsh, G S, Byers, P H
Format: Artigo
Sprog:Inglês
Udgivet: National Academy of Sciences 1981
Fag:
Online adgang:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC320349/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/6946461/
https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.78.8.5142
Tags: Tilføj Tag
Ingen Tags, Vær først til at tagge denne postø!