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Bardet-Biedl syndrome with end-stage kidney disease in a four-year-old Romanian boy: a case report

BACKGROUND: Bardet-Biedl syndrome is a significant genetic cause of chronic kidney disease in children. Kidney abnormalities are a major cause of morbidity and mortality in Bardet-Biedl syndrome, but the onset of end-stage renal disease at an early age and continuous ambulatory peritoneal dialysis,...

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Détails bibliographiques
Auteurs principaux: Mihai, Cristina M, Marshall, Jan D, Stoicescu, Ramona M
Format: Artigo
Langue:Inglês
Publié: BioMed Central 2011
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC3174128/
https://ncbi.nlm.nih.gov/pubmed/21843323
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1752-1947-5-378
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