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Bardet–Biedl syndrome: A rare cause of end stage renal disease

Bardet–Biedl syndrome is a rare autosomal recessive disorder, recently categorized as ciliopathy characterized by dysfunction of primary cilia which results in myriad manifestations in various organ systems. Though renal abnormalities can occur in this syndrome, renal failure is a rare presentation....

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Dades bibliogràfiques
Publicat a:Int J Appl Basic Med Res
Autor principal: Hemachandar, R
Format: Artigo
Idioma:Inglês
Publicat: Medknow Publications & Media Pvt Ltd 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4318109/
https://ncbi.nlm.nih.gov/pubmed/25664275
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/2229-516X.149254
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