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Respiratory Complex III Is Required to Maintain Complex I in Mammalian Mitochondria

A puzzling observation in patients with oxidative phosphorylation (OXPHOS) deficiencies is the presence of combined enzyme complex defects associated with a genetic alteration in only one protein-coding gene. In particular, mutations in the mtDNA encoded cytochrome b gene are associated either with...

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Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Acín-Pérez, Rebeca, Bayona-Bafaluy, María Pilar, Fernández-Silva, Patricio, Moreno-Loshuertos, Raquel, Pérez-Martos, Acisclo, Bruno, Claudio, Moraes, Carlos T., Enríquez, José A.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2004
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3164363/
https://ncbi.nlm.nih.gov/pubmed/15053874
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