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Role of von Hippel-Lindau protein in fibroblast proliferation and fibrosis

Idiopathic pulmonary fibrosis (IPF) is characterized by exaggerated fibroblast proliferation and accumulation of collagens and fibronectin. The extracellular fibronectin and collagen network is regulated by von Hippel-Lindau protein (pVHL). However, it is unknown whether pVHL contributes to pulmonar...

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Autores principales: Zhou, Qiyuan, Pardo, Annie, Königshoff, Melanie, Eickelberg, Oliver, Budinger, G. R. Scott, Thavarajah, Krishna, Gottardi, Cara J., Jones, Jonathan, Varga, John, Selman, Moises, Sznajder, Jacob I., Raj, J. Usha, Zhou, Guofei
Formato: Artigo
Lenguaje:Inglês
Publicado: Federation of American Societies for Experimental Biology 2011
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3157679/
https://ncbi.nlm.nih.gov/pubmed/21642472
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1096/fj.10-177824
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