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Current Concepts of Hyperinflammation in Chronic Granulomatous Disease

Chronic granulomatous disease (CGD) is the most common inherited disorder of phagocytic functions, caused by genetic defects in the leukocyte nicotinamide dinucleotide phosphate (NADPH) oxidase. Consequently, CGD phagocytes are impaired in destroying phagocytosed microorganisms, rendering the patien...

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Detalhes bibliográficos
Main Authors: Rieber, Nikolaus, Hector, Andreas, Kuijpers, Taco, Roos, Dirk, Hartl, Dominik
Formato: Artigo
Idioma:Inglês
Publicado em: Hindawi Publishing Corporation 2012
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3144705/
https://ncbi.nlm.nih.gov/pubmed/21808651
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2012/252460
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