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Facioscapulohumeral muscular dystrophy region gene 1 (FRG1) is a dynamic RNA-associated and actin bundling protein

Facioscapulohumeral muscular dystrophy (FSHD) region gene 1 (FRG1) is a dynamic nuclear and cytoplasmic protein that, in skeletal muscle, shows an additional localization to the sarcomere. Maintaining appropriate levels of FRG1 protein is critical for the muscle and vascular development in the verte...

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Autors principals: Jessica Sun, Chia-Yun, van Koningsbruggen, Silvana, Long, Steven W., Straasheijm, Kirsten, Klooster, Rinse, Jones, Takako I., Bellini, Michel, Levesque, Lyne, Brieher, William M., van der Maarel, Silvère M., Jones, Peter L.
Format: Artigo
Idioma:Inglês
Publicat: 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3143299/
https://ncbi.nlm.nih.gov/pubmed/21699900
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jmb.2011.06.014
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