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Oral and Dental Phenotype of Dyskeratosis Congenita

Dyskeratosis congenita (DC) is an inherited bone marrow failure syndrome that is characterized by lacey reticular hyperpigmentation of the skin, dystrophic nails, mucous membrane leukoplakia and pancytopenia. Diagnosis may be delayed until clinical signs are apparent. Severe pancytopenia frequently...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awduron: Atkinson, Jane C., Harvey, Kristen E., Domingo, Demetrio L., Trujillo, Maria I., Guadagnini, Jean-Pierre, Gollins, Sherri, Giri, Neelam, Hart, Thomas C., Alter, Blanche P.
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: 2008
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC3142998/
https://ncbi.nlm.nih.gov/pubmed/18938267
Tagiau: Ychwanegu Tag
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