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Lung tissues in systemic sclerosis have gene expression patterns unique to pulmonary fibrosis and pulmonary hypertension

OBJECTIVE: Pulmonary complications in systemic sclerosis (SSc), including pulmonary fibrosis (PF) and pulmonary arterial hypertension (PAH), are the leading cause of mortality. We compared the molecular fingerprint of SSc lung tissues and matching primary lung fibroblasts to those of normal donors,...

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Autori principali: Hsu, Eileen, Shi, Haiwen, Jordan, Rick M., Lyons-Weiler, James, Pilewski, Joseph M., Feghali-Bostwick, Carol A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2011
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3139818/
https://ncbi.nlm.nih.gov/pubmed/21360508
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/art.30159
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