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Alterations of lipid metabolism in Wilson disease

INTRODUCTION: Wilson disease (WD) is an inherited disorder of human copper metabolism, characterised by accumulation of copper predominantly in the liver and brain, leading to severe hepatic and neurological disease. Interesting findings in animal models of WD (Atp7b(-/- )and LEC rats) showed altere...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Seessle, Jessica, Gohdes, Annina, Gotthardt, Daniel Nils, Pfeiffenberger, Jan, Eckert, Nicola, Stremmel, Wolfgang, Reuner, Ulrike, Weiss, Karl Heinz
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: BioMed Central 2011
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3127787/
https://ncbi.nlm.nih.gov/pubmed/21595966
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1476-511X-10-83
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