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Structural model of the TRPP2/PKD1 C-terminal coiled-coil complex produced by a combined computational and experimental approach

Autosomal dominant polycystic kidney disease (ADPKD) is caused by mutations in TRPP2 and PKD1, which form an ion channel/receptor complex containing three TRPP2 and one PKD1. A TRPP2 C-terminal coiled-coil trimer, critical for the assembly of this complex, associates with a single PKD1 C-terminal co...

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Autors principals: Zhu, Jiang, Yu, Yong, Ulbrich, Maximilian H., Li, Ming-hui, Isacoff, Ehud Y., Honig, Barry, Yang, Jian
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 2011
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3121833/
https://ncbi.nlm.nih.gov/pubmed/21642537
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1017669108
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