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Evidence that Proteosome Inhibitors and Chemical Chaperones Can Rescue the Activity of Retinol Dehydrogenase 12 mutant T49M

Retinol dehydrogenase 12 (RDH12) is a microsomal enzyme that catalyzes the reduction of all-trans-retinaldehyde to all-trans-retinol when expressed in cells. Mutations in RDH12 cause severe retinal degeneration; however, some of the disease-associated RDH12 mutants retain significant catalytic activ...

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Библиографические подробности
Главные авторы: Lee, Seung-Ah, Belyaeva, Olga V., Kedishvili, Natalia Y.
Формат: Artigo
Язык:Inglês
Опубликовано: 2011
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC3086964/
https://ncbi.nlm.nih.gov/pubmed/21232531
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.cbi.2011.01.001
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