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Libyan Boy with Autosomal Recessive Trait (P22-phox Defect) of Chronic Granulomatous Disease

Chronic granulomatous disease (CGD) is a primary immune deficiency disorder of the phagocytes. In this disorder, phagocytic cells (polymorphonuclear leukocytes and monocytes) cannot produce active oxygen metabolites and, therefore, cannot destroy the ingested intracellular bacteria. Clinically, pati...

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Autores principales: Al-Bousafy, Ahmed, Al-Tubuly, Abdulhamid, Dawi, Elhassan, Zaroog, Salem, Schulze, Ilka
Formato: Artigo
Lenguaje:Inglês
Publicado: CoAction Publishing 2006
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3081356/
https://ncbi.nlm.nih.gov/pubmed/21526014
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4176/060905
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