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Residual NADPH Oxidase and Survival in Chronic Granulomatous Disease
BACKGROUND: Failure to generate phagocyte-derived superoxide and related reactive oxygen intermediates (ROIs) is the major defect in chronic granulomatous disease, causing recurrent infections and granulomatous complications. Chronic granulomatous disease is caused by missense, nonsense, frameshift,...
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| Autors principals: | , , , , , , , , , , , , , |
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| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
2010
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3069846/ https://ncbi.nlm.nih.gov/pubmed/21190454 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1056/NEJMoa1007097 |
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