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Residual NADPH Oxidase and Survival in Chronic Granulomatous Disease

BACKGROUND: Failure to generate phagocyte-derived superoxide and related reactive oxygen intermediates (ROIs) is the major defect in chronic granulomatous disease, causing recurrent infections and granulomatous complications. Chronic granulomatous disease is caused by missense, nonsense, frameshift,...

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Autors principals: Kuhns, Douglas B., Alvord, W. Gregory, Heller, Theo, Feld, Jordan J., Pike, Kristen M., Marciano, Beatriz E., Uzel, Gulbu, DeRavin, Suk See, Long Priel, Debra A., Soule, Benjamin P., Zarember, Kol A., Malech, Harry L., Holland, Steven M., Gallin, John I.
Format: Artigo
Idioma:Inglês
Publicat: 2010
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3069846/
https://ncbi.nlm.nih.gov/pubmed/21190454
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1056/NEJMoa1007097
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