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New developments in the treatment of hyperammonemia: emerging use of carglumic acid

Hyperammonemia is a true neonatal emergency with high toxicity for the central nervous system and developmental delay. The causes of neonatal hyperammonemia are genetic defects of urea cycle enzymes, organic acidemias, lysinuric protein intolerance, hyperammonemia–hyperornithinemia– homocitrullinemi...

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Detalles Bibliográficos
Main Authors: Daniotti, Marta, la Marca, Giancarlo, Fiorini, Patrizio, Filippi, Luca
Formato: Artigo
Idioma:Inglês
Publicado: Dove Medical Press 2011
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3056327/
https://ncbi.nlm.nih.gov/pubmed/21403788
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2147/IJGM.S10490
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