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Review: Transactive response DNA-binding protein 43 (TDP-43): mechanisms of neurodegeneration

Since the identification of phosphorylated and truncated transactive response DNA-binding protein 43 (TDP-43) as a primary component of ubiquitinated inclusions in amyotrophic lateral sclerosis (ALS) and frontotemporal lobar degeneration with ubiquitin-positive inclusions, and the discovery that mut...

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Autori principali: Gendron, T. F., Josephs, K. A., Petrucelli, L.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3052765/
https://ncbi.nlm.nih.gov/pubmed/20202122
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/j.1365-2990.2010.01060.x
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