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Altered chloride metabolism in cultured cystic fibrosis skin fibroblasts.

An abnormal regulation of chloride permeability has been described for epithelial cells from patients with cystic fibrosis (CF). To learn more about the biochemical basis of this inherited disease, we have studied chloride metabolism in cultured CF fibroblasts by comparing the efflux of 36Cl- from m...

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Detalles Bibliográficos
Publicado en:Proc Natl Acad Sci U S A
Autores principales: Mattes, P M, Maloney, P C, Littlefield, J W
Formato: Artigo
Lenguaje:Inglês
Publicado: National Academy of Sciences 1987
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Acceso en línea:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC304790/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/3472247/
https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.84.9.3009
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