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Altered chloride metabolism in cultured cystic fibrosis skin fibroblasts.

An abnormal regulation of chloride permeability has been described for epithelial cells from patients with cystic fibrosis (CF). To learn more about the biochemical basis of this inherited disease, we have studied chloride metabolism in cultured CF fibroblasts by comparing the efflux of 36Cl- from m...

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Autors principals: Mattes, P M, Maloney, P C, Littlefield, J W
Format: Artigo
Idioma:Inglês
Publicat: 1987
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC304790/
https://ncbi.nlm.nih.gov/pubmed/3472247
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