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A 556 kb deletion in the downstream region of the PAX6 gene causes familial aniridia and other eye anomalies in a Chinese family

PURPOSE: The paired box gene 6 (PAX6) on human chromosome 11p13 is an essential transcription factor for eye formation in animals. Mutations in PAX6 can lead to varieties of autosomal-dominant ocular malformations with aniridia as the major clinical signs. Known genetic alterations causing haplo-ins...

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Autors principals: Cheng, Fang, Song, Wulian, Kang, Yang, Yu, Shihui, Yuan, Huiping
Format: Artigo
Idioma:Inglês
Publicat: Molecular Vision 2011
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3038207/
https://ncbi.nlm.nih.gov/pubmed/21321669
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