Mammalian Frataxin: An Essential Function for Cellular Viability through an Interaction with a Preformed ISCU/NFS1/ISD11 Iron-Sulfur Assembly Complex

BACKGROUND: Frataxin, the mitochondrial protein deficient in Friedreich ataxia, a rare autosomal recessive neurodegenerative disorder, is thought to be involved in multiple iron-dependent mitochondrial pathways. In particular, frataxin plays an important role in the formation of iron-sulfur (Fe-S) c...

Descrición completa

Gardado en:
Detalles Bibliográficos
Main Authors: Schmucker, Stéphane, Martelli, Alain, Colin, Florent, Page, Adeline, Wattenhofer-Donzé, Marie, Reutenauer, Laurence, Puccio, Hélène
Formato: Artigo
Idioma:Inglês
Publicado: Public Library of Science 2011
Assuntos:
Research Article
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3027643/
https://ncbi.nlm.nih.gov/pubmed/21298097
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0016199
Tags: Engadir etiqueta
Sen Etiquetas, Sexa o primeiro en etiquetar este rexistro!

Títulos similares