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Glycopeptide storage in skin fibroblasts cultured from a patient with alpha-mannosidase deficiency.

Patients with mannosidosis, an inherited deficiency of lysosomal alpha-mannosidase, accumulate large amounts of mannose-rich oligosaccharides (the "core" of the carbohydrate units of many glocoproteins) in brain and liver and excrete these partial degradation products in their urine. A pro...

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Bibliografische gegevens
Hoofdauteurs: Tsay, G C, Dawson, G, Matalon, R
Formaat: Artigo
Taal:Inglês
Gepubliceerd in: 1975
Onderwerpen:
Online toegang:https://ncbi.nlm.nih.gov/pmc/articles/PMC301920/
https://ncbi.nlm.nih.gov/pubmed/125765
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