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Persistent testicular delta5-isomerase-3beta-hydroxysteroid dehydrogenase (delta5-3beta-HSD) deficiency in the delta5-3beta-HSD form of congenital adrenal hyperplasia.

A partial testicular defect in testosterone secretion has been documented in a pubertal male with a congenital adrenal hyperplasia due to hereditary deficiency of the delta5-isomerase-3beta-hydroxysteroid dehydrogenase enzyme complex (delta5-3beta-HSD). Diagnosis of the enzymatic defect is based on...

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Bibliografski detalji
Glavni autori: Schneider, G, Genel, M, Bongiovanni, A M, Goldman, A S, Rosenfield, R L
Format: Artigo
Jezik:Inglês
Izdano: 1975
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC301803/
https://ncbi.nlm.nih.gov/pubmed/164481
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