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Fibrinogen Philadelphia. A hereditary hypodysfibrinogenemia characterized by fibrinogen hypercatabolism.

A new, autosomally inherited abnormal fibrinogen associated with hypofibrinogenemia has been described in several members of a family. Plasma fibrinogen measured either as thrombin-clottable protein or by immunodiffusion revealed a fibrinogen level ranging between 60 and 90 mg/100 ml. The thrombin t...

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Pubblicato in:J Clin Invest
Autori principali: Martinez, J, Holburn, R R, Shapiro, S S, Erslev, A J
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Clinical Investigation 1974
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Accesso online:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC301504/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/11344575/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI107595
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