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A Mouse Model of Generalized non-Herlitz Junctional Epidermolysis Bullosa

Epidermolysis bullosa (EB) is a class of intractable, rare, genetic disorders characterized by fragile skin and blister formation as a result of dermal-epidermal mechanical instability. EB presents with considerable clinical and molecular heterogeneity. Viable animal models of junctional epidermolys...

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Detaylı Bibliyografya
Asıl Yazarlar: Bubier, Jason A., Sproule, Thomas J., Petell, Lydia, Webb, Cameron, Fine, Jo-David, Roopenian, Derry C., Sundberg, John P.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: 2010
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC3010368/
https://ncbi.nlm.nih.gov/pubmed/20336083
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/jid.2010.46
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