Wordt geladen...

Normal and Friedreich Ataxia Cells Express Different Isoforms of Frataxin with Complementary Roles in Iron-Sulfur Cluster Assembly

Friedreich ataxia (FRDA) is an autosomal recessive degenerative disease caused by insufficient expression of frataxin (FXN), a mitochondrial iron-binding protein required for Fe-S cluster assembly. The development of treatments to increase FXN levels in FRDA requires elucidation of the steps involve...

Volledige beschrijving

Bewaard in:
Bibliografische gegevens
Hoofdauteurs: Gakh, Oleksandr, Bedekovics, Tibor, Duncan, Samantha F., Smith, Douglas Y., Berkholz, Donald S., Isaya, Grazia
Formaat: Artigo
Taal:Inglês
Gepubliceerd in: American Society for Biochemistry and Molecular Biology 2010
Onderwerpen:
Online toegang:https://ncbi.nlm.nih.gov/pmc/articles/PMC2992281/
https://ncbi.nlm.nih.gov/pubmed/20889968
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M110.145144
Tags: Voeg label toe
Geen labels, Wees de eerste die dit record labelt!