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Liver Cirrhosis in a Patient with Sickle Cell Trait (Hb Sβ(+) Thalassemia) without Other Known Causes of Hepatic Disease

Liver involvement in patients with sickle cell anemia/trait includes a wide range of alterations, from mild liver function test abnormalities to cirrhosis and acute liver failure. Approximately 15–30% of patients with sickle cell anemia present cirrhosis at autopsy. The pathogenesis of cirrhosis is...

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Autors principals: Santi, Luca, Montanari, Giancarlo, Berardi, Sonia, Patti, Corrado, Frigerio, Marta, Sama, Claudia, Caraceni, Paolo, Bernardi, Mauro
Format: Artigo
Idioma:Inglês
Publicat: S. Karger AG 2009
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2988917/
https://ncbi.nlm.nih.gov/pubmed/21103241
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000235235
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