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A novel recessive GUCY2D mutation causing cone–rod dystrophy and not Leber's congenital amaurosis

Cone–rod dystrophies are inherited retinal dystrophies that are characterized by progressive degeneration of cones and rods, causing an early decrease in central visual acuity and colour vision defects, followed by loss of peripheral vision in adolescence or early adult life. Both genetic and clinic...

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Autores principales: Ugur Iseri, Sibel A, Durlu, Yusuf K, Tolun, Aslihan
Formato: Artigo
Lenguaje:Inglês
Publicado: Nature Publishing Group 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2987461/
https://ncbi.nlm.nih.gov/pubmed/20517349
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/ejhg.2010.81
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