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“Laminopathies:” a wide spectrum of human diseases

Mutations in genes encoding the intermediate filament nuclear lamins and associated proteins cause a wide spectrum of diseases sometimes called “laminopathies.” Diseases caused by mutations in LMNA encoding A-type lamins include autosomal dominant Emery-Dreifuss muscular dystrophy and related myopat...

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Autors principals: Worman, Howard J., Bonne, Gisèle
Format: Artigo
Idioma:Inglês
Publicat: 2007
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2964355/
https://ncbi.nlm.nih.gov/pubmed/17467691
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.yexcr.2007.03.028
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