Intravenous administration of phosphorylated acid alpha-glucosidase leads to uptake of enzyme in heart and skeletal muscle of mice.

Benzer Materyaller

• The conservative substitution Asp-645-->Glu in lysosomal alpha-glucosidase affects transport and phosphorylation of the enzyme in an adult patient with glycogen-storage disease type II.
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  Yazar:: Hoefsloot, L H, ve diğerleri
  Baskı/Yayın Bilgisi: (1988)