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Restricted heterogeneity of T lymphocytes in combined immunodeficiency with hypereosinophilia (Omenn's syndrome).

We report the immunological characteristics of five patients with Omenn's syndrome, a rare inherited immunodeficiency also known as combined immunodeficiency with hypereosinophilia. The syndrome is characterized by T cell infiltration of skin, gut, liver, and spleen leading to diffuse erythrode...

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Autores principales: de Saint-Basile, G, Le Deist, F, de Villartay, J P, Cerf-Bensussan, N, Journet, O, Brousse, N, Griscelli, C, Fischer, A
Formato: Artigo
Lenguaje:Inglês
Publicado: 1991
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC295173/
https://ncbi.nlm.nih.gov/pubmed/2010548
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