A carregar...

Cloning and expression of mutations demonstrating intragenic complementation in mut0 methylmalonic aciduria.

The mut0 mutation resulting in methylmalonyl CoA mutase (MCM) apoenzyme deficiency and methylmalonic aciduria is characterized by undetectable enzyme activity in cell extracts and low incorporation of propionate into cultured cells which is not stimulated by hydroxycobalamin. A mut0 fibroblast cell...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Main Authors: Qureshi, A A, Crane, A M, Matiaszuk, N V, Rezvani, I, Ledley, F D, Rosenblatt, D S
Formato: Artigo
Idioma:Inglês
Publicado em: 1994
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC294249/
https://ncbi.nlm.nih.gov/pubmed/7909321
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!