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Friedreich Ataxia: Molecular Mechanisms, Redox Considerations, and Therapeutic Opportunities

Mitochondrial dysfunction and oxidative damage are at the origin of numerous neurodegenerative diseases like Friedreich ataxia and Alzheimer and Parkinson diseases. Friedreich ataxia (FRDA) is the most common hereditary ataxia, with one individual affected in 50,000. This disease is characterized by...

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Main Authors: Santos, Renata, Lefevre, Sophie, Sliwa, Dominika, Seguin, Alexandra, Camadro, Jean-Michel, Lesuisse, Emmanuel
Formato: Artigo
Idioma:Inglês
Publicado: Mary Ann Liebert, Inc. 2010
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC2924788/
https://ncbi.nlm.nih.gov/pubmed/20156111
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1089/ars.2009.3015
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