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Friedreich Ataxia: Molecular Mechanisms, Redox Considerations, and Therapeutic Opportunities

Mitochondrial dysfunction and oxidative damage are at the origin of numerous neurodegenerative diseases like Friedreich ataxia and Alzheimer and Parkinson diseases. Friedreich ataxia (FRDA) is the most common hereditary ataxia, with one individual affected in 50,000. This disease is characterized by...

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Main Authors: Santos, Renata, Lefevre, Sophie, Sliwa, Dominika, Seguin, Alexandra, Camadro, Jean-Michel, Lesuisse, Emmanuel
Format: Artigo
Jezik:Inglês
Izdano: Mary Ann Liebert, Inc. 2010
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC2924788/
https://ncbi.nlm.nih.gov/pubmed/20156111
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1089/ars.2009.3015
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