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Cystathionine γ-Lyase-deficient Mice Require Dietary Cysteine to Protect against Acute Lethal Myopathy and Oxidative Injury

Cysteine is considered a nonessential amino acid in mammals as it is synthesized from methionine via trans-sulfuration. However, premature infants or patients with hepatic failure may require dietary cysteine due to a lack of cystathionine γ-lyase (CTH), a key trans-sulfuration enzyme. Here, we gene...

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Main Authors: Ishii, Isao, Akahoshi, Noriyuki, Yamada, Hidenori, Nakano, Shintaro, Izumi, Takashi, Suematsu, Makoto
Formato: Artigo
Idioma:Inglês
Publicado: American Society for Biochemistry and Molecular Biology 2010
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC2924062/
https://ncbi.nlm.nih.gov/pubmed/20566639
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M110.147439
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