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A Case of Hermansky-Pudlak Syndrome with Pulmonary Sarcoidosis

Hermansky-Pudlak syndrome is an autosomal recessive disorder of lysosomal storage characterized by the triad of occulocutaneous albinism, bleeding diathesis, and pulmonary fibrosis. Sarcoidosis is a disease characterized by the development of noncaseating granulomas, most commonly affecting the lung...

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Détails bibliographiques
Auteurs principaux: Gruson, Lisa, Berk, Thomas
Format: Artigo
Langue:Inglês
Publié: Matrix Medical Communications 2009
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC2923935/
https://ncbi.nlm.nih.gov/pubmed/20725574
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