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Suppression of the novel ER protein Maxer by mutant ataxin-1 in Bergman glia contributes to non-cell-autonomous toxicity

Non-cell-autonomous effect of mutant proteins expressed in glia has been implicated in several neurodegenerative disorders, whereas molecules mediating the toxicity are currently not known. We identified a novel molecule named multiple α-helix protein located at ER (Maxer) downregulated by mutant at...

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Autori principali: Shiwaku, Hiroki, Yoshimura, Natsue, Tamura, Takuya, Sone, Masaki, Ogishima, Soichi, Watase, Kei, Tagawa, Kazuhiko, Okazawa, Hitoshi
Natura: Artigo
Lingua:Inglês
Pubblicazione: Nature Publishing Group 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2910266/
https://ncbi.nlm.nih.gov/pubmed/20531390
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/emboj.2010.116
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