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Distinct Roles for Laminin Globular Domains in Laminin α1 Chain Mediated Rescue of Murine Laminin α2 Chain Deficiency

BACKGROUND: Laminin α2 chain mutations cause congenital muscular dystrophy with dysmyelination neuropathy (MDC1A). Previously, we demonstrated that laminin α1 chain ameliorates the disease in mice. Dystroglycan and integrins are major laminin receptors. Unlike laminin α2 chain, α1 chain binds the re...

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Autori principali: Gawlik, Kinga I., Åkerlund, Mikael, Carmignac, Virginie, Elamaa, Harri, Durbeej, Madeleine
Natura: Artigo
Lingua:Inglês
Pubblicazione: Public Library of Science 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2906511/
https://ncbi.nlm.nih.gov/pubmed/20657839
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0011549
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